Table III.

Clinical data and outcome for the 10 individual HLH patients.

Patient	1	2	3	4	5	6	7	8	9	10
Time to diagnosisa	23	20	10	19	17	17	16	29	60	52
HLH-2004b	–	–	–	+	+	+	–	–	–	+
Therapy	–	–	CTX	CTX	CTX	AVT	Dx	AVT	ATD, Dx	IVIG
Outcomec	Dead at d0	Dead d+10	Dead d+22	Dead d+108	Dead d+36	Dead at+73	Alive	Alive	Alive	Dead d+18

^aTime to diagnosis defined as time (days) from admission to hospital to HLH diagnosis.

^bHLH-2004 defined as treatment according to the HLH-2004 protocol.

^cOutcome defined as number of days from HLH diagnosis.

+ = Yes; – = No; ATD = Anti-tuberculous drugs; AVT = Antiviral therapy; CTX = Chemotherapy; Dx = Dexamethasone; IVIG = Intravenous immunoglobulins; HLH = Haemophagocytic lymphohistiocytosis.