Table 1.

Demographic, clinical, and laboratory characteristics at initial presentation of the study population

Variables		Findings
Age at initial presentation (year)		4.3 (2.0–14.0)
Gender ratio (Male/Female)		68/62 (1.1:1.0)
Age at onset (year)		3.9 (1.2–12.0)
Positive family history; n (%)		4 (3.1)
Body weight percentile; n (%)	< 5th centile	5 (3.8)
	> 95th centile	7 (5.4)
Hemoglobin, gm/dL		12.0±1.2
Blood urea, mg/dL		34.5 (8.0–140.0)
Serum creatinine, mg/dL		0.7 (0.1–2.6)
Serum albumin, g/dL		1.5 (0.4–2.5)
Urine albumin/creatinine ratio		4.6 (0.6–52.2)
Serum cholesterol, mg/dL		430 (210–913)
C3, mg/dL		110 (20–180)
C4, mg/dL		29 (8–96)