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. 2016 Apr 15;263:71–81. doi: 10.1007/s00415-015-7930-1

Table 3.

Proposed terminology for inner ear diseases related to endolymphatic hydrops, based on clinical and imaging findings

Proposed new terminology Old terminology Other terms
Primary hydropic ear disease (PHED)
 Cochleovestibular type Definite MD Typical MD
SSNHL+V
 Cochlear type Cochlear MD FLFSNHL
ALFSNHL
 Vestibular type Vestibular MD RPV, Forme fruste
Secondary hydropic ear disease (SHED)
 Cochlear/vestibular/cochleovestibular type, associated with: Secondary MD Menière syndrome
  VS
  LVAS
  Labyrinthitis, meningitis
  Noise induced hearing loss
  Trauma
  Congenital hearing loss DEH
  Inner ear malformation
 …

FLSNHL fluctuating low frequency sensorineural hearing loss, ALFSNHL acute low frequency sensorineural hearing loss, RPV recurrent peripheral vestibulopathy, SSNHL+V sudden sensorineural hearing loss with vertigo, DEH delayed endolymphatic hydrops, VS vestibular schwannoma, LVAS large vestibular aquaeduct syndrome