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. 1997 Jun;77(6):576–578. doi: 10.1136/hrt.77.6.576

Coronary involvement in the Churg-Strauss syndrome.

S Hellemans 1, J Dens 1, D Knockaert 1
PMCID: PMC484806  PMID: 9227307

Abstract

The Churg-Strauss syndrome (CSS) is a rare systemic disease characterised by vasculitis and peripheral eosinophilia in patients with an atopic constitution. Cardiac involvement is an important cause of morbidity and mortality yet coronary involvement is very rarely documented. We report the case of a 38 year old man presenting with fulminant heart failure. Coronary arteriography demonstrated extensive focal vasculopathy consistent with vasculitis. The diagnosis of CSS was established based upon the classical diagnostic criteria and corticosteroid treatment resulted in a spectacular remission of disease activity.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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