Table 1.
Summary table for retroperitoneal lipomatosis.
| Etiology | Sporadic development of non-encapsulated lipomas in retroperitoneum. Associated with multiple symmetric lipomatosis. |
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| Incidence | 1.7 cases per 100,000 population. |
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| Gender ratio | Male to female ratio is 18:1. |
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| Age predilection | 4th to 5th decade |
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| Risk factor | Black race |
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| Treatment | Conservative and follow-up in mild or asymptomatic cases. Surgical excision with or without urinary tract interventions (stenting, ureterostomy). |
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| Prognosis | Progressive and non-curable nature of disease causing varying degree of urinary tract obstruction eventually leading to end stage renal disease if not treated. Patients subjected to excision with or without urinary diversion lead symptom free life. Life time risk of urinary bladder malignancy. |
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| Imaging findings | |
| Plain Radiographs | Extensive lucent areas in abdomen and pelvis. |
| Sonography | Diffuse hyperechoic mass causing sleeve like encasement of retroperitoneal organs along with their displacement and cigar shaped elongated and floating bladder in pelvis. |
| Intravenous urography | Varying degree of hydronephrosis and hydroureter. Urinary bladder is elongated in shape. |
| Barium enema | Elongated, straightened rectum with enlarged pre sacral space. |
| CT scan | Non enhancing fat density diffuse mass in retroperitoneum with few fibrous septations within it. |
| MRI scan | Homogenously hyperintense retroperitoneal lesion on both T1W and T2W sequences and showing suppression of signal on fat saturated sequences. No enhancement on post contrast images. |