Table 1.

Baseline characteristics of study patients (at time of analysis)

Characteristics	N = 77
Male	77 (100%)
Current age (years)	14.1 ± 6.4 (range 3–35)
Current number of non-ambulatory subjects	48 (62%)
Mean age of loss of ambulation	10.6 ± 2.0 (range 7–16)
Current subjects with LV dysfunction	25 (33%)
Mean age of onset of LV dysfunction	15.4 ± 4.7 (range 8–27)
Medications
Current or previous corticosteroids	78% (N=60)
Duration corticosteroids (years)	3.4 ± 2.5
Current or previous ACEi*	48% (N=37)
Duration ACEi (years)	2.9 ± 2.9
Current or previous ARB†	12% (N=9)
Duration ARB (years)	3.9 ± 1.8
Current or previous beta blocker	30% (N=23)
Duration beta blocker (years)	3.3 ± 2.0
Current or previous mineralocorticoid	4% (N=3)
Duration of mineralocorticoid (years)	2 ± 1.8
Current skeletal muscle strength
Median subjective arm strength	4
Median subjective leg strength	4 minus
Mean QMT‡ (pounds)	73.1 ± 39.6

^*Angiotensin converting enzyme inhibitor (ACEi)

^†Angiotensin receptor blocker (ARB)

^‡Quantitative muscle testing (QMT)