. Author manuscript; available in PMC: 2017 Feb 1.

Published in final edited form as: Respir Physiol Neurobiol. 2015 Nov 28;222:11–15. doi: 10.1016/j.resp.2015.11.013

Table 1.

Characteristics of the sample

Subject	Sex	Age (years)	Age at diagnosis (years)	Max. Inspiratory Pressure (cm H₂O)	Forced Vital Capacity (% predicted)	Ambulation	Ventilatory support
Pompe
P1	Female	14	10	62	87	Community	None
P2	Female	18	14	49	86	Community	None
P3	Female	38	35	52	60	Household	None
P4	Female	41	39	52	79	Community	Nighttime
P5	Female	46	40	50	89	Community	Nighttime
P6	Female	25	24	30	23	Community	Nighttime
P7	Male	48	35	13	10	Non-Ambulatory	Fulltime
P8	Female	43	30	20	15	Non-Ambulatory	Fulltime

Average		34.2 ± 13.3	38.4 ± 11.4	41 ± 18	56 ± 34

Controls
C1	Female	42	-	85	90	-	-
C2	Male	35	-	125	96	-	-
C3	Female	31	-	80	89	-	-
C4	Female	23	-	105	107	-	-

Average		32.5 ± 8.3		98 ± 21	96 ± 9