Figure 1. Chromatograms of five de novo mutations and the corresponding fundus pictures of the affected probands.
The sequence variations are marked with red circles. OD and OS represent right and left eyes, respectively. (a) chromatograms and fundus pictures of a 4-month-old male with the c.511C>G (p.L171V) mutation. (b) chromatograms and fundus pictures of a 1-year-old female with the splicing mutation c.790-2A>C. (c) chromatograms and fundus pictures of a 7-year-old female with c.1573C>T (p.Q525*) mutation. (d) chromatograms and fundus pictures of a 10-month-old female with a c.2524C>T (p.Q842*) mutation. (e) chromatograms and fundus pictures of a 1-year-old male with a c.2807C>G (p.S936*) mutation. Notice the existence of chorioretinopathy in panel a (both eyes); the falciform retinal folds in panels a (OS), b (OD), c (OD), d (OS) and e (both eyes); the retrolenticular fibrotic masses in panels c (OS), d (OS) and e (both eyes); cataracts and microphthalmia in panel d (OD); dragged disc and macular in panels a (OD) and b (OS).