Table 1.
Potential etiology based on retinal arteriole- or venule-predominance of retinal vasculitis.
| Primarily retinal arteritis | Primarily retinal phlebitis | Arteritis and phlebitis |
|---|---|---|
| Systemic lupus erythematosus |
Sarcoidosis | Relapsing polychondritis* |
| Polyarteritis nodosa | Multiple sclerosis | GPA * |
| Syphilis | Pars planitis | Crohn’s disease/UC* |
| Toxoplasmosis | Behçet’s disease | Frosted branch angiitis |
| HSV/VZV | Birdshot chorioretinopathy | Tuberculosis |
| IRVAN | HIV associated retinal vasculitis |
|
| Churg-Strauss syndrome* | Eales disease | |
| Susac syndrome |
HSV: herpes simplex virus; VZV: varicella zoster virus; IRVAN: idiopathic retinal vasculitis, aneurysms, and neuroretinitis; HIV: human immunodeficiency virus; GPA: granulomatosis with polyangiitis; UC: ulcerative colitis.
These diseases are rare causes of retinal vasculitis so characterization is based on a small number of descriptions.