Table 2.

Classification of systemic mastocytosis (modified form Valent et al. 2007)

Categories of systemic mastocytosis (SM)	Subtypes
Indolent systemic mastocytosis	• Smoldering systemic mastocytosis • Isolated bone marrow mastocytosis • Well-differentiated systemic mastocytosis
Aggressive systemic mastocytosis (ASM)	• ASM in transformation
Systemic mastocytosis with an associated clonal hematological non-mast cell lineage disease	• SM-acute myeloid leukemia • SM-myelodysplastic syndrome • SM-myeloproliferative neoplasm • SM-chronic myelomonocytic leukemia • SM-chronic eosinophilic leukemia • SM-non-Hodgkin lymphoma • SM-multiple myeloma