. 2015 Jul 29;3(2):e1074332. doi: 10.1080/23723556.2015.1074332

Table 1.

Human proteins containing 2 (Cx₉C) and 2 (Cx₃C) motifs^*.

Symbol	Synonyms	Accession number	Cysteine motif	Function^#	Chromosomal location
CHCHD1	FLJ25854	NP_976043	Cx₉C-Cx₉C	Mitochondrial translation	10q22.3
CHCHD3	MINOS3; Mic19	NP_060282.1	Cx₉C-Cx₉C	MICOS complex	7q33
CHCHD6	CHCM1; Mic25	NP_115719.1	Cx₉C-Cx₉C	MICOS complex	3q21.3
CHCHD4	MIA40; TIMM40	NP_001091972.1	Cx₉C-Cx₉C	IMS redox-regulated import	3p25.1
CHCHD10	N27C7–4	NP_001288268.1	Cx₉C-Cx₉C	Cristae morphology	22q11.23
NDUFA8	PGIV	NP_055037.1	Cx₉C-Cx₉C	CI subunit	9q33.2
NDUFB7	B18	NP_004137.2	Cx₉C-Cx₉C	CI subunit	19p13.12
NDUFS5	CI-15k	NP_001171908.1	Cx₉C-Cx₉C	CI subunit	1p34.3
UQCRH	QCR6	AAH93060	Cx₁₀C-Cx₉C	CIII subunit	1p34.1
COX6B1	COXG	NP_001854.1	Cx₉C-Cx₁₀C	CIV subunit	19q13.12
COX6B2	CT59	NP_653214.2	Cx₉C-Cx₁₀C	CIV subunit	19q13.42
COX17		NP_005685.1	Cx₉C-Cx₉C	CIV copper chaperone	3q13.33
COX19	MGC104475	NP_001026788	Cx₉C-Cx₉C	CIV copper chaperone	7p22.3
CHCHD7	COX23	NP_001011668	Cx₉C-Cx₉C	CIV copper chaperone	8q11.23
COA4	CMC3; E2IG2	NP_057649.2	Cx₉C-Cx₉C	CIV assembly factor	11q13.4
COA5	FLJ27524; Pet191	NP_001008216	Cx₉C-Cx₁₀C	CIV assembly factor	2q11.2
COA6		NP_001013003.1	Cx₉C-Cx₁₀C	CIV assembly factor	1q42.2
CMC1	MGC61571	NP_872329	Cx₉C-Cx₉C	CIV biogenesis	3p24–1
CMC2	MGC45036; DC13	NP_064573	Cx₉C-Cx₉C	CIV biogenesis	16q23.2
CHCHD2		NP_057223	CX₉C-CX₉C	CIV subunit expression and assembly	7p11.2
TRIAP1	MDM35	NP_057483	Cx₉C-Cx₉C	Mitochondrial lipid homeostasis	12q24.31
CHCHD5	MIC14	NP_115685.1	Cx₉C-Cx₉C	Unknown	2q14.1
CMC4	P8MTCP1	NP_001018024.1	Cx₉C-Cx₉C	Unknown	Xq28
UPF0545		NP_776154	Cx₉C-Cx₉C	Unknown	22q11.21
C17orf89		NP_001079990.1	Cx₉C-Cx₉C	Unknown	17q25.3
TIMM8A	DDP1	NP_001139423.1	Cx₃C-Cx₃C	Protein import	Xq22.1
TIMM8B	DDP2	NP_036591.2	Cx₃C-Cx₃C	Protein import	11q23.1
TIMM9	TIM9A	NP_001291414.1	Cx₃C-Cx₃C	Protein import	14q23.1
TIMM10	TIM10A	NP_036588.1	Cx₃C-Cx₃C	Protein import	11q12.1
TIMM10B	TIM10B; Tim9B	NP_036324.1	Cx₃C-Cx₃C	Protein import	11p15.4
TIMM13	Tim13	NP_036590.1	Cx₃C-Cx₃C	Protein import	19p13.3

Data have been extracted from References 8 to 10, as well as from public databases.

CI, respiratory chain complex CI; CIII, respiratory chain complex CIII; CIV, respiratory chain complex CIV; IMS, intermembrane space; MICOS, mitochondrial contact site.