| BN-PAGE | blue native polyacrylamide gel electrophoresis |
| ATP | adenosine triphosphate |
| ADP | adenosine diphosphate |
| mtDNA | mitochondrial DNA |
| MMP | mitochondrial membrane potential |
| ROS | reactive oxygen species |
| OXPHOS | oxidative phosphorylation system |
| cyt c | cytochrome c |
| ETC | electron transfer chain |
| NDUFS3 | NADH dehydrogenase (ubiquinone) iron-sulfur protein 3 |
| CAP | chloramphenicol |
| MELAS | mitochondrial encephalopathy, lactic acidosis, and stroke-like episode |
| NDUFA13/Grim19 | NADH dehydrogenase (ubiquinone) 1 α subcomplex, 13 |
| ND1 | NADH dehydrogenase subunit 1 |
| SCAFs | supercomplex assembly factors |
| Rcf1/2 | respiratory supercomplex factors 1 and 2 |
| COX7a21 | cyt c oxidase subunit 7A-related protein |
| DDM | N-dodecyl-β-d-maltoside |
| NBT | nitrotetrazolium blue chloride |
| DAB | 3,3’-diamiobenzidine tetra hydrochloride hydrate |
| BCIP | 5-bromo-4-chloro-3’-indolyphosphate p-toluidine |
| TMRM | Tetramethylrhodamine methyl ester |