Table 1.
Confidence level for IgG4-RD indication according to type of organ involved
| Types of organ involved | Confidence for indication of IgG4-RD |
|---|---|
| Only one type of involved organ | |
| Salivary glands/lacrimal glands (MD) | Strong |
| Hepatobiliary-pancreatic-splenic | Moderate |
| Retroperitoneal/mediastinal fibrosis | Moderate |
| Regional or systemic lymphadenopathy | Weak |
| Respiratory system (sinus/lung parenchymal/airway/pleura) | Weak |
| Urinary system (kidney/ureter/bladder/prostate) | Weak |
| Two types of involved organs | |
| MD + respiratory system | Strong |
| MD + pancreatic-hepatobiliary-splenic | Strong |
| MD + one other type of organ | Moderate |
| Retroperitoneal/mediastinal fibrosis + pancreatic-hepatobiliary-splenic | Moderate |
| Two other types of organs | Weak |
| Three types of involved organs | |
| MD + pancreatic-hepatobiliary-splenic + respiratory system | Strong |
| MD + pancreatic-hepatobiliary-splenic + retroperitoneal/mediastinal fibrosis | Strong |
| MD + pancreatic-hepatobiliary-splenic + urinary | Moderate |
| MD + two other organ types involved | Moderate |
| Three other organ types involved | Weak |
| Multi-type organ involvement | |
| MD + greater than or equal to three types of organs involved | Strong |
| Other multi-type organ involvement | Moderate |
MD: Mikulicz's disease; IgG4-RD: Immunoglobulin G4-related disease.