Table 1.
Patient and tumor characteristics by site of presentation.
| Characteristic | Patient and tumor characteristics by site* | ||||
|---|---|---|---|---|---|
| Neck (n=16) | Paranasal sinus (n=3) | Scalp/face (n=27) | Supraclavicular (n=2) | Total (N=48) | |
| Age at diagnosis, y | |||||
| Median | 48.8 | 74.4 | 70.0 | 27.6 | 68.5 |
| Range | (19.1-85.6) | (41.8-82.6) | (23.5-86.9) | (25.9-29.2) | (19.1-86.9) |
| Sex | |||||
| Female | 4 (25.0) | 1 (33.3) | 9 (33.3) | 0 (0.0) | 14 (29.2) |
| Male | 12 (75.0) | 2 (66.7) | 18 (66.6) | 2 (100.0) | 34 (70.8) |
| Presentation | |||||
| Recurrent | 5 (31.3) | 0 (0.0) | 4 (14.8) | 1 (50.0) | 10 (20.8) |
| Primary | 11 (68.8) | 3 (100.0) | 23 (85.2) | 1 (50.0) | 38 (79.2) |
| Histologic finding | |||||
| DFSP | 1 (6.3) | 0 (0.0) | 0 (0.0) | 0 (0.0) | 1 (2.1) |
| Leiomyosarcoma | 2 (12.5) | 0 (0.0) | 3 (11.1) | 0 (0.0) | 5 (10.4) |
| MPNST | 0 (0.0) | 0 (0.0) | 1 (3.7) | 0 (0.0) | 1 (2.1) |
| MFH/UPS | 3 (18.8) | 0 (0.0) | 4 (14.8) | 2 (100.0) | 9 (18.8) |
| Spindle cell | 2 (12.5) | 0 (0.0) | 2 (7.4) | 0 (0.0) | 4 (8.3) |
| Synovial sarcoma | 5 (31.3) | 0 (0.0) | 1 (3.7) | 0 (0.0) | 6 (12.5) |
| Angiosarcoma | 0 (0.0) | 1 (25.0) | 13 (48.1) | 0 (0.0) | 14 (29.2) |
| Liposarcoma | 1 (6.3) | 0 (0.0) | 2 (7.4) | 0 (0.0) | 3 (6.3) |
| Other° | 2 (12.5) | 1 (25.0) | 0 (0.0) | 0 (0.0) | 3 (6.3) |
| Hemangiopericytoma | 0 (0.0) | 1 (25.0) | 1 (3.7) | 0 (0.0) | 2 (4.2) |
| Rhabdomyosarcoma | 0 (0.0) | 1 (25.0) | 0 (0.0) | 0 (0.0) | 1 (2.1) |
| Grade | |||||
| Low | 2 (12.5) | 0 (0.0) | 4 (14.8) | 0 (0.0) | 6(12.5) |
| High | 7 (43.8) | 1 (33.3) | 18 (66.8) | 2 (100.0) | 28 (58.3) |
| Not available | 7 (43.8) | 2 (66.7) | 5 (18.5) | 0 (0.0) | 14 (29.1) |
| Size, cm | |||||
| ≤5 | 11 (68.8) | 3 (100.0) | 17 (63.0) | 2 (100.0) | 33 (68.8) |
| >5 | 5 (31.3) | 0 (0.0) | 10 (37.0) | 0 (0.0) | 15 (31.2) |
| Depth | |||||
| Superficial | 2 (12.5) | 0 (0.0) | 16 (59.3) | 1 (50.0) | 19 (39.6) |
| Deep | 14 (87.5) | 3 (100.0) | 11 (40.3) | 1 (50.0) | 29 (60.4) |
DFSP, dermatofibrosarcoma protuberans; MFH, malignant fibrous histiocytoma; MPNST, malignant peripheral nerve sheath tumor; UPS, unclassified pleomorphic sarcoma.
*Values are presented as number and percentage of patients unless specified otherwise.
°Other histologic findings include interdigitating dendritic cell sarcoma, chordoma, and hemangioendothelioma.