Table 2.
Symptom and Actionable Transmission Data by Patient
Patient | Clinical Diagnosis | Actionable Data (No. Transmissions) | If Actionable Data, What Was Rhythm and Resultant Action? | Symptom Events (No. Transmissions) | If Symptom Event, What Was the Rhythm? |
---|---|---|---|---|---|
1 | LQTS | None | n/a | Yes (3) | NSR×2; ST |
2 | LQTS | None | n/a | Yes (1) | ST |
3 | LQTS | None | n/a | Yes (6) | ST×6 |
4 | LQTS | None | n/a | Yes (2) | ST×2 |
5 | LQTS | None | n/a | Yes (5) | NSR×5 |
6 | LQTS | None | n/a | None | n/a |
7 | LQTS | None | n/a | None | n/a |
8 | LQTS | Yes (1) | Tightly coupled ventricular couplet→Activity Restrictions | Yes (2) | ST; Tightly coupled ventricular couplet |
9 | CPVT | None | n/a | Yes (6) | ST×3; NSR w/ventricular bigeminy; ST w/isolated PVCs×2 |
10 | CPVT | None | n/a | Yes (2) | ST×2 |
11 | CPVT | None | n/a | Yes (1) | ST |
12 | CPVT | None | n/a | Yes (1) | ST |
13 | CPVT | Yes (2) |
Polymorphic VT→Initiate of β‐blocker AT→Uptitrate of β‐blocker |
None | n/a |
14 | CPVT | Yes (4) |
Sinus pauses, bidirectional ventricular coupletsàInitiate atenolol Nonsustained VT→Encourage medication compliance Significant sinus pauses→Wean β‐blockers Polymorphic VT→Explant ILR; Implant ICD |
Yes (1) | TdP |
15 | CPVT | Yes (1) | Multifocal PVCs→Initiate nadolol | Yes (2) | ST; NSR w/ventricular trigeminy |
16 | CPVT | Yes (3) |
Multifocal PVCs→Uptitrate nadolol Bidirectional VT→Initiate Flecainide Bidirectional Ventricular CoupletsàUptitrate flecainide |
Yes (4) | Bidirectional VT; NSR w/ventricular bigeminy×2; NSR w/isolated PVCs |
17 | CPVT | None | n/a | None | n/a |
18 | ARVC | Yes (1) | Sinus pause→Wean β‐blocker | Yes (1) | ST |
19 | ARVC | None | n/a | Yes (1) | ST |
20 | BrS | None | n/a | Yes (4) | ST×3; NSR |
Both symptom and actionable data by patent are presented. Details about transmission data are provided. ARVC indicates arrhythmogenic right ventricular cardiomyopathy; AT, atrial tachycardia; BrS, Brugada syndrome; CPVT, catecholaminergic polymorphic ventricular tachycardia; ICD, implantable cardioverter defibrillator; ILR, ; LQTS, long QT syndrome; n/a, not applicable; NSR, normal sinus rhythm; PVCs, premature ventricular contractions; ST, sinus tachycardia; TdP, Torsades de Pointes; VT, ventricular tachycardia.