Table 3.
Reports of tracheobronchial compression by enlarged pulmonary artery in adults (≥ 16 years old) with PAH.
| Study, year, ref | Ref | n | Age (years) | Gender | Type of PAH | PAH-specific therapy | Site of compression | Size of PA (cm) |
|---|---|---|---|---|---|---|---|---|
| Edwards et al 1960 | [4] | 2 | 24,N/A | M,N/A | ASD,PDA | No | left tracheal border, LB, RMB, LUB | N/A |
| Perloff et al 2003 | [34] | 1 | 54 | M | VSD | No | RMB | N/A |
| Achouh et al 2008 | [30] | 2 | 34,56 | 2 M | Mesenterico-caval shunt, ASD | Yes | LB,2 RB | N/A |
| Arimura et al 2015 | [70] | 1 | 42 | F | I PAH | Yes | LB | 7.9 |
Abbreviations: ASD: atrial septal defect, IPAH: idiopathic pulmonary arterial hypertension, LB: left main stem bronchus, LUB: left upper lobe bronchus, N/A: not available, PA: pulmonary artery, PDA: patent ductus arteriosus, PHA: pulmonary arterial hypertension, Ref: reference, RB: right main stem bronchus, RMB: right middle bronchus, VSD: ventricular septal defect.