Table 2. Involuntary Movements as the Presenting Motor Abnormality.

	Distribution of Movements
Chorea
Ataxia–telangiectasia	Limbs ± face and trunk
AOA1
AOA2
Friedreich’s ataxia
Dystonia
Ataxia–telangiectasia	Limbs (young children); cervical, upper limbs (older children)
AVED	Cervical, upper limbs most common
AOA2	Upper limbs
Dystonia with myoclonus
Ataxia–telangiectasia	Cervical, upper limbs
AVED
Postural tremor
AVED	Head
AOA2

Abbreviations: AOA, Ataxia with Oculomotor Apraxia; AVED, Ataxia with Vitamin E Deficiency.