Table 1.

Clinical features of 25 cases of epithelioid inflammatory myofibroblastic sarcoma

Case	Age/Sex	Site	Size (cm)	Multifocal	Treatment	Recurrence	Metastasis	Follow up	Source
1	7y/M	Abdominal cavity	NA	No	SE, CT	Yes (5w, 5 m)	No	NED(5 m)	Ma et al. [7]
2	7 m/M	Mesentery and omentum	11	Yes	SE	Yes (8 m)	No	AWD(8 m)
3	2y/M	Retroperitoneal and abdominal cavity	10	No	SE	No	No	NED(36 m)	Patel et al. [6]
4	34y/M	Liver	8	No	SE	Yes (5 m)	No	DOD(5.5 m)	Chen et al. [8]
5	44y/M	Omentum	NA	Yes	SE, CT, ALKi	Yes (5 m)	Liver (12 m)	AWD(39 m)	Butrynski et al. [9]
6	41y/M	Omentum	26	Yes	ST, CT, ALKi	Yes (12 m)	Liver(12 m)	NED(40 m)	Marino-Enriquez et al. [4]
7	59y/M	Mesentery of small bowel	15	Yes	SE, CT	Yes	No	DOD (12 m)
8	6y/M	Omentum	10.5	No	SE, CT	Yes	No	AWD(3 m)
9	28y/M	Mesentery of small bowel	NA	Yes	NA	NA	NA	NA
10	63y/M	Mesentery of small bowel	25	No	SE, CT	Yes	No	DOD(3 m)
11	42y/M	Intra-abdominal	NA	No	SE, CT	Yes	No	AWD(13 m)
12	7 m/M	Peritoneum	10	No	SE, CT, RT	Yes	No	DOD(36 m)
13	40y/M	Peritoneum	8	No	SE, CT, RT	Yes	Lung, liver, and lymph node
14	31y/M	Mesentery of small bowel	17.5	Yes	SE, CT	Yes	No	DOD(11 m)
15	6y/M	Omentum and mesentery	14	Yes	SE	NA	NA	NA
16	39y/M	Mesentery of small bowel	15	Yes	SE	NA	NA	NA
17	57y/M	Pleura or chest wall	NA	NA	ALKi	NA	NA	NA	Kozu et al. [10]
18	19y/F	Mesentery of small bowel	19	No	SE	Yes(9w)	No	DOD(12w)	Li et al. [11]
19	39y/M	Mesentery of colon	15	No	SE, CT	Yes(4 m)	No	AWD(12 m)
20	22y/M	Mesentery of small bowel	6	Yes	SE, CT, ALKi	Yes(3 m, 4 m)	No	AWD(14 m)	Kimbara et al. [12]
21	37/F	Rectum	5	No	SE	No(8 m)	No	NED(8 m)	Current cases
22	55/M	Mesentery of ileum	11	No	SE, CT	Yes(2 m)	No	NED(10 m)
23	22/M	Mesentery of colon	20	Yes	SE, ALKi	Yes(2 m)	No	AWD(14 m)
24	58/F	Omentum	5.5	No	SE, CT	Yes(2 m)	No	DOD(8 m)
25	15/F	Transverse colon	12	No	SE	No(7 m)	No	NED(7 m)

ALKi ALK inhibitor, AWD alive with disease, CE cholecystectomy, CT chemotherapy, DOD dead of disease, NA not available, NED no evidence of disease, RT radiation therapy, SE surgical excision