[Table/Fig-9]:

PAPVC-Superior and inferior pulmonary veins: Important Facts.

PAPVC	One or more (but not all) pulmonary veins drain into RA or its venous tributaries like SVC, IVC, left innominate vein and coronary sinus [5]
Subtypes	Left pulmonary veins drain either into left innominate vein or coronary sinus. Associated with ASD. Right pulmonary veins may drain into SVC (associated with sinus venosus ASD) or into IVC (Scimitar syndrome or venolobar sequestration)
Incidence	Seen in <1% of all CHDs.
Association	ASD Broncho-pulmonary sequestration (scimitar syndrome)
Syndromes	Scimitar syndrome = right PAPVC + hypoplastic right lung + hypoplastic RPA + right lower lobe sequestration
Imaging Features (Plain)	Cardiomegaly- RA/RV dilatation	Dilated SVC	“Scimitar sign” produced by an anomalous pulmonary vein that drains any or all of the lobes of the right lung. Seen as crescent shaped vertical shadow, curves outward along the right cardiac border, usually from the middle of the lung to the cardiophrenic angle Resembles Turkish/Persian sword (=scimitar)
Imaging Features (Specific)	Echo direct demonstration of PAPVC; inability to visualize all pulmonary veins with RA/RV dilatation – strongly suggests PAPVC MRI in unclear pulmonary venous anatomy CT preferred in scimitar syndrome.
Management	Surgical correction (ligation & re-anastamosis)