Table 1.

Branched-chain Amino Acid Levels in Plasma (μmoles/liter ± S.D.)
	Wild type	Heterozygote	Frogleg
leucine	131.8 ± 8.9	110.7 ± 11.4	30.2 ± 8.5
isoleucine	57.0 ± 5.2	48.7 ± 7.4	10.8 ± 2.9
valine	132.0 ± 12.9	114.0 ± 18.6	39.0 ± 7.2