Table 5.
Treatment variables at initial visit for subjects with confirmed VLCAD deficiency after identification by newborn screening 1
| Recommended/Prescribed Treatment (n=number of responses)2 |
Yes, % (n) |
|---|---|
| Emergency protocol ± Sick day plan (n=51) | 98% (50) |
| Cornstarch (n=40) | 10% (4) |
| Essential Fatty Acids (n=40) | 23% (9) |
| Fat-Restricted Diet (n=41) | 85% (35) |
| MCT supplementation (n=32) | 75% (24) |
| L-Carnitine (n=21) | 100% (21) |
1
Data collected from subjects within 6 months of their initial study visit, ages 2.7 ± 2.5 years (Range 0.03 to 11.4 years).
2
For each variable, n is total number of subjects with available data to indicate if the treatment was prescribed or not; next column gives percent of these subjects who received the listed treatment.