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. 2016 Jul 28;2016:4235898. doi: 10.1155/2016/4235898

Table 1.

Epigenetic mechanisms in cognition and IDDs.

Epigenetic changes Writers Erasers Readers Effect on gene expression Effects on cognition IDDs involved
5mC DNMTs TETs
AID/Apobec
MBPs Repression Memory formation [17, 18]
Memory consolidation [24]
Rett Syndrome [25]

mCH DNMT3a TETs
AID/Apobec
MBPs
(e.g., MeCP2)
Repression Rett Syndrome [26]

5hmC TETs Activation Memory formation [22]
Memory extinction [23]
LTD [23]

Histone acetylation HATs HDACs (HDAC1–5, SIRT1) CPB
BRDs
Activation Memory formation [27]
Memory consolidation [28, 29]
Depression [30]
Fear extinction [31]
Rubinstein-Taybi syndrome [32, 33]

Histone methylation HMTs (MLL, GLP/G9a) HDMs (LSD1, JMJD1a) Chromodomains (e.g., HP1) Activation/repression Memory formation [34]
Memory consolidation [35]
Adaptive behaviour [36]
Kleefstra syndrome [37, 38]
Sotos syndrome [39]
Wolf-Hirschhorn syndrome [40]
Kabuki syndrome [41, 42]
Weaver syndrome 2 [43]
Claes-Jensen-type syndromic X-linked ID [44]
Siderius X-linked ID [45]

Chromatin remodelling nBAF, ATRX Activation/repression Long-term memory formation [46] Coffin-Siris Syndrome [47]
Nicolaides-Baraitser syndrome [48]
ATRX syndrome [49]
ASD [50]