Table 1.
Patient | 1 | 2 | 3 |
---|---|---|---|
Age, y | 41 | 45 | 43 |
Age of diagnosis, y | 40 | 44 | 43 |
Race | White | White | White |
Recurrent pneumothorax | Yes | No | Yes |
History of chylothorax | No | Yes | No |
History of pleurodesis | No | Yes | No |
FEV1 (% predicted) | 105 | 104 | 80 |
RV (% predicted) | 99 | 55 | 124 |
RV/TLC ratio | 0.35 | 0.23 | 0.41 |
Lung diffusion capacity CO2 (% predicted) | 102 | 91 | 86 |
Peak VO2 (% predicted) | 76 | 83 | 170 |
Peak Heart Rate (% predicted) | 97 | 93 | 96 |
Peak SaO2 (%) | 99 | 94 | 95 |
Pneumothorax after PFT | Yes | Possibly related | No |
Pneumothorax after CPET | No | Possibly related | Yes |
Treated with pleurodesis | Yes | No | Yes |
CPET = cardiopulmonary exercise testing; FEV1 = forced expiratory volume in the first second; PFT = pulmonary function testing; RV = residual volume; RV/TLC = ratio between RV and TLC; SaO2 = pulse oxygen saturation; TLC = total lung capacity; VO2 = oxygen uptake.