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Table 1.

Patient characteristics

Median or count Range or percentage
Sex, female 21/57 36.8%
Age at diagnosis, y 60 40-78
β2 microglobulin at diagnosis >3, mg/L 19/46 41.3%
Age at biopsy, y 62 41-83
Familial history of WM 3/57 5.3%
Splenomegaly 13/57 22.8%
Lymphadenopathy 30/57 52.6%
Bone marrow involvement, % 60 5-95
Hemoglobin, g/dL 11.1 8.2-14.5
Serum IgM, mg/dL 3750 416-8320
Serum IgG, mg/dL 517 82-3890
Serum IgA, mg/dL 40 6-516
MYD88 mutations 52/57 91.2%
CXCR4 mutations 23/57 40.0%
ARID1A mutations 5/51 9.8%
CD79B mutations 4/51 7.8%
Deletion chromosome 6q 24/53 45.3%
Amplification chromosome 6p 6/53 11.3%
Amplification chromosome 3q 11/52 19.2%
Amplification chromosome 4 10/52 21.1%