Table 1:

Patient characteristics

Age at revision	Median age of 17.9 years (range, 4.6–38.1 years)
Interval from original Fontan operation	Median 13.8 years (range, 2.1–25.4 years)
Gender, n (%)	Male 14 (66.7), female 7 (33.3)
Original diagnoses, n (%)	TA: 10 (47.6), DORV: 5 (23.8), ccTGA: 2 (9.5) PA with IVS: 1 (4.8), Heterotaxy: 2 (9.5), TGA, VSD, PS: 1 (4.8)
Heart rhythm
NSR, n (%)	10 (47.6)
A fib., n (%)	5 (23.8)
A flutter, n (%)	3 (14.3)
Atrial tachycardia, n (%)	2 (9.5)
CAVB with PPM, n (%)	1 (4.8)
Causes of revision
Dilated RA, n (%)	15 (71.4)
Arrhythmia, n (%)	8 (38.1)
RA thrombi, n (%)	6 (28.6)
PLE, n (%)	3 (14.3)
AVVR, n (%)	5 (23.8)
Fenestration, n (%)	7 (33.3)
Arrhythmia surgery, n (%)	8 (38.1)

TA: tricuspid atresia; DORV: double outlet right ventricle; ccTGA: congenitally corrected transposition of great arteries; PA with IVS: pulmonary atresia with intact ventricular septum; TGA: transposition of great arteries; VSD: ventricular septal defect; PS: pulmonary stenosis; NSR: normal sinus rhythm; A fib.: atrial fibrillation; A flutter: atrial flutter; CAVB: complete atrioventricular block; PPM: permanent pacemaker; RA: right atrium; PLE: protein-losing enteropathy; AVVR: atrioventricular valve regurgitation.