Table 1. Main haemostatic findings of the VWD patients with quantitative VWF defects studied.
| VWD type | No subjects/Families | VWF:Ag(U/dL) | VWF:CB(U/dL) | VWF:RCo(U/dL) | VWF:FVIIIB (U/dL) | FVIII(U/dL) | FVIII/VWF:Ag | Platelet VWF(U/dL) | BS | |
|---|---|---|---|---|---|---|---|---|---|---|
| Mild type 1 | Normal-platelet-VWF | 20/8 | 37.9±11.2 | 35.2±13.3 | 35.9±11.6 | 33.9±10.8 | 47.4±14.1 | 1.3±0.3 | 96.4±18.0 | 4.8±4.1 |
| Low-platelet-VWF | 44/32 | 33.6±9.2 | 32.0±11.2 | 31.8±11.0 | 32.2±10.5 | 56.8±21.9 | 1.9±1.1 | 47.2±15.9 | 3.8±3.4 | |
| Severe type 1 | 8/7 | 5.9±2.4 | 4.0±1.72 | 7.1±3.7 | 6.1±1.83 | 32.2±17.8 | 5.2±1.8 | 4.8±2.7 | 11.5±4.1 | |
| Type 3 | 5/3 | ND | ND | ND | ND | 4.5±2.2 | ND | ND | 24±4.8 | |
| Type Vicenza | 16/10 | 10.7±6.2 | 9.4±4.8 | 10.6±6.9 | 9.6±5.3 | 20.3±8.9 | 2.0±0.8 | 93.8±25.1 | 9.7±4.0 | |
| Normal range | 60–160 | 65–150 | 60–130 | 65–150 | 60–160 | 0.75–1.2 | 70–140 | 0–5 | ||
ND = not detectable; BS = bleeding score from BAT (bleeding assessment tool).