Table 1. Clinical manifestations of this pedigree with Basan syndrome.

	Skin blistering	Congenital milia	Lack of fingerprints	Contractures of digits	Hypohidrosis	PPK	Nail dystrophy	Hyperpigmentation	Knuckle pads
II:3	+	+	+	Severe	+	Severe	+	+	Mild
III:1	+	+	+	Moderate	+	Moderate	−	+	Mild
III:4	+	+	+	Severe	+	−	−	+	Severe
III:6	+	+	+	Mild	+	−	−	−	−
IV:1	+	+	+	Mild	+	−	−	+	Severe
IV:2	+	+	+	Mild	+	−	−	+	Moderate
IV:4	+	+	+	Mild	+	−	−	−	Severe
IV:5	+	+	+	Mild	+	−	−	−	Severe

Abbreviation: PPK, palmoplantar keratoderma.