Table 3.

Incidences of hyperammonemic events with a peak ammonia ≥ 500 μmol/L, maximum analysis period 550 days

Parameter	CPS1D	OTCD	ASSD	All patients
Number of patients	12	23	27	63
Type of hyperammonemic event
▪ no event ≥ 500 μmol/L	3	6	10	19
▪ at least one event ≥ 500 μmol/L, patient alive	5	7	13	26
individual number of events ≥ 500 μmol/L
1	3	6	10	20
2	1	1	2	4
3	1	–	1	2
▪ at least one event ≥ 500 μmol/L, patient died	4	10	4	18
individual number of events ≥ 500 μmol/L
1	4	9	2	15
2	–	1	–	1
3	–	–	1	1
4	–	–	1	1