Table 1.
Patient characteristics.
| Age/sex | Clinical presentation | Initial diagnosis | Time from onset to diagnosis | MRI findings | EEG findings | CSF 14-3-3 | Autopsy |
|---|---|---|---|---|---|---|---|
| 82/F | Memory impairment, aphasia, and depression | Alzheimer’s dementia | 7 weeks | Small vessel disease | Generalized slowing | Positive | Positive |
| 54/F | Confusion, ataxia, and falls | Hepatic encephalopathy | 6 weeks | DWI and FLAIR basal ganglia hyperintensity | Periodic sharp wave complexes | Positive | Positive |
| 58/F | Confusion, myoclonus, urinary incontinence, ataxia, and Parkinsonism | CJD | 10 weeks | DWI and FLAIR hyperintensity in basal ganglia and pulvinar nuclei of the thalami | Periodic sharp wave complexes | Positive | Not done |
| 67/M | Headache, blurred vision, ataxia, personality change, confusion, and myoclonus | Subacute encephalitis | 9 weeks | DWI and FLAIR hyperintensity in basal ganglia and left frontal cortex | Periodic sharp wave complexes and slow background | Positive | Positive |