TABLE 1.
Patient Baseline Characteristics
Patient | Sex | Age at Diagnosis | Phenotype | Location | Symptoms/Signs | Previous Interventions |
---|---|---|---|---|---|---|
Pediatric LMs | ||||||
1 | M | Prenatal | Mixed macrocystic and microcystic LMs | Retroperitoneum | Edema | Debulking |
Pelvis | Lymphatic drainage | |||||
Perineum | Bleeding | |||||
Left lower extremity | Sepsis | |||||
Nonambulatory status | ||||||
2 | M | 5 y | Generalized lymphatic anomaly | Diffuse | Edema | Diuretics |
Pleural/pericardial effusions Sepsis | Debulking | |||||
3 | M | 11 y | Lymphedema | Left foot | Lymphedema | None |
Recurrent cellulitis | ||||||
KTS | ||||||
4 | F | Prenatal | Capillary, venous, and LMs | Right lower extremity Peritoneum | Edema | Sclerotherapy |
Lymphatic drainage | ||||||
Bleeding | ||||||
Sepsis | ||||||
5 | M | At birth | Capillary, venous, and LMs | Left lower extremity Perineum | Edema in toes | Debulking |
Leakage from old incisions | Embolization of vein of Servelle | |||||
Pain | ||||||
Prenatal LMs | ||||||
6 | F | Prenatal | Mixed macrocystic and microcystic LMs | Cervicofacial | Prenatal radiographic finding | None |
Concern for airway compromise |
F, female; M, male.