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. 2016 Sep;138(3):e20154545. doi: 10.1542/peds.2015-4545

TABLE 1.

Patient Baseline Characteristics

Patient Sex Age at Diagnosis Phenotype Location Symptoms/Signs Previous Interventions
Pediatric LMs
1 M Prenatal Mixed macrocystic and microcystic LMs Retroperitoneum Edema Debulking
Pelvis Lymphatic drainage
Perineum Bleeding
Left lower extremity Sepsis
Nonambulatory status
2 M 5 y Generalized lymphatic anomaly Diffuse Edema Diuretics
Pleural/pericardial effusions Sepsis Debulking
3 M 11 y Lymphedema Left foot Lymphedema None
Recurrent cellulitis
KTS
4 F Prenatal Capillary, venous, and LMs Right lower extremity Peritoneum Edema Sclerotherapy
Lymphatic drainage
Bleeding
Sepsis
5 M At birth Capillary, venous, and LMs Left lower extremity Perineum Edema in toes Debulking
Leakage from old incisions Embolization of vein of Servelle
Pain
Prenatal LMs
6 F Prenatal Mixed macrocystic and microcystic LMs Cervicofacial Prenatal radiographic finding None
Concern for airway compromise

F, female; M, male.