Table 1.

Respiratory-Chain Activities in Muscle Mitochondria, Muscle Homogenate, and Fibroblasts

	Muscle Mitochondria				Muscle Homogenate		Fibroblasts
S1	C	S2	C	S3	C	S1	C	S2	C	S3	C
CI/CS	0.03a	0.47–1.54	0.02a	0.14–0.19	0.02a	0.12–0.22	0.05a	0.16–0.60	ND	0.11–0.17	ND	0.12–0.26
CII/CS	0.21	0.13–0.35	0.28	0.23–0.29	0.26	0.24–0.38	0.53	0.34–0.89	0.36	0.24–0.30	0.31	0.25–0.34
CIII/CS	0.84	0.70–1.76	5.05	3.44–4.66	ND	2.29–3.64	0.87	0.57–1.38	2.03	2.37–3.06	3.30	2.24–2.97
CIV/CS	1.01	0.47–1.84	2.49	1.65–2.19	1.42	1.24–1.97	0.43	0.29–0.95	0.86	1.13–1.48	1.70	1.14–1.54
CV/CS	ND	ND	1.40	0.66–0.94	ND	0.46–0.97	0.72	0.20–0.82	0.20	0.21–0.29	ND	0.23–0.33

Abbreviations are as follows: CI–CV, complexes I–V, respectively; CS, citrate synthase; S1–S3, subjects S1–S3, respectively; C, control values; and ND, not done.

^aAbnormal values.