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. Author manuscript; available in PMC: 2018 Jan 1.
Published in final edited form as: Transplantation. 2017 Jan;101(1):131–140. doi: 10.1097/TP.0000000000001076

Table 2. Causes of end-organ disease requiring liver or intestine transplantation in 214 study subjects.

Diagnoses Liver-containing allografts Diagnoses Intestine containing allografts
Biliary Atresia 48 Volvulus 14
Maple syrup urine disease 22 Gastroschisis 12
Hepatoblastoma 13 Necrotizing enterocolitis 9
Fulminant Liver Failure 9 Jejunal Atresia 6
Crigler Najjar Syndrome 7 Hirschsprung's 4
Familial cholestasis 7 Pseudoobstruction 4
Urea cycle defect 7 Tufting enteropathy 2
Cystic Fibrosis 6 Trauma 2
Cryptogenic Cirrhosis 5 Microvillous inclusion disease 2
ARKPD 4 SMV thrombosis 1
Autoimmune hepatitis 4
Primary Scelorisn Cholangitis 4
Alagille's syndrome 4
Caroli's disease 3
Tyrosinemia 3
Wilson's disease 2
Alpha 1 antitrypsin deficiency 2
Neonatal hepatitis 2
Embryonal sarcoma 1
Histiocytosis 1
Neuroendocrine tumor 1
Rhabdomyosarcoma 1
Histiocytosis 1
abernathy 1
TOTAL 158 56