Table 2. Causes of end-organ disease requiring liver or intestine transplantation in 214 study subjects.
Diagnoses | Liver-containing allografts | Diagnoses | Intestine containing allografts |
---|---|---|---|
Biliary Atresia | 48 | Volvulus | 14 |
Maple syrup urine disease | 22 | Gastroschisis | 12 |
Hepatoblastoma | 13 | Necrotizing enterocolitis | 9 |
Fulminant Liver Failure | 9 | Jejunal Atresia | 6 |
Crigler Najjar Syndrome | 7 | Hirschsprung's | 4 |
Familial cholestasis | 7 | Pseudoobstruction | 4 |
Urea cycle defect | 7 | Tufting enteropathy | 2 |
Cystic Fibrosis | 6 | Trauma | 2 |
Cryptogenic Cirrhosis | 5 | Microvillous inclusion disease | 2 |
ARKPD | 4 | SMV thrombosis | 1 |
Autoimmune hepatitis | 4 | ||
Primary Scelorisn Cholangitis | 4 | ||
Alagille's syndrome | 4 | ||
Caroli's disease | 3 | ||
Tyrosinemia | 3 | ||
Wilson's disease | 2 | ||
Alpha 1 antitrypsin deficiency | 2 | ||
Neonatal hepatitis | 2 | ||
Embryonal sarcoma | 1 | ||
Histiocytosis | 1 | ||
Neuroendocrine tumor | 1 | ||
Rhabdomyosarcoma | 1 | ||
Histiocytosis | 1 | ||
abernathy | 1 | ||
TOTAL | 158 | 56 |