Table 2. Causes of end-organ disease requiring liver or intestine transplantation in 214 study subjects.
| Diagnoses | Liver-containing allografts | Diagnoses | Intestine containing allografts |
|---|---|---|---|
| Biliary Atresia | 48 | Volvulus | 14 |
| Maple syrup urine disease | 22 | Gastroschisis | 12 |
| Hepatoblastoma | 13 | Necrotizing enterocolitis | 9 |
| Fulminant Liver Failure | 9 | Jejunal Atresia | 6 |
| Crigler Najjar Syndrome | 7 | Hirschsprung's | 4 |
| Familial cholestasis | 7 | Pseudoobstruction | 4 |
| Urea cycle defect | 7 | Tufting enteropathy | 2 |
| Cystic Fibrosis | 6 | Trauma | 2 |
| Cryptogenic Cirrhosis | 5 | Microvillous inclusion disease | 2 |
| ARKPD | 4 | SMV thrombosis | 1 |
| Autoimmune hepatitis | 4 | ||
| Primary Scelorisn Cholangitis | 4 | ||
| Alagille's syndrome | 4 | ||
| Caroli's disease | 3 | ||
| Tyrosinemia | 3 | ||
| Wilson's disease | 2 | ||
| Alpha 1 antitrypsin deficiency | 2 | ||
| Neonatal hepatitis | 2 | ||
| Embryonal sarcoma | 1 | ||
| Histiocytosis | 1 | ||
| Neuroendocrine tumor | 1 | ||
| Rhabdomyosarcoma | 1 | ||
| Histiocytosis | 1 | ||
| abernathy | 1 | ||
| TOTAL | 158 | 56 |