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. Author manuscript; available in PMC: 2017 Nov 1.
Published in final edited form as: Semin Cell Dev Biol. 2016 Mar 5;59:118–125. doi: 10.1016/j.semcdb.2016.03.001

Table 1.

Mouse mutants with de-silencing of retrotransposons (LINE1 and/or IAP) in male germ cells

Protein Mutant phenotype De-repressed retrotransposons References
piRNA pathway factors
PIWIL2 (MILI) Meiotic arrest LINE1 and IAP [57, 98]
PIWIL1 (MIWI) Spermiogenic arrest LINE1 [53]
PIWIL4 (MIWI2) Meiotic arrest LINE1 and IAP [23, 57]
MOV10L1 Meiotic arrest LINE1 and IAP [38, 99]
DDX4 (MVH) Meiotic arrest LINE1 and IAP [100]
TDRD1 Meiotic arrest LINE1 [31, 101]
TDRD5 Spermiogenic arrest LINE1 (incomplete penetrance) [102]
TDRD9 Meiotic arrest LINE1 [27]
TDRD12 Meiotic arrest LINE1 and IAP [28]
TDRKH Meiotic arrest LINE1 [50]
PLD6 Meiotic arrest LINE1 [103]
ASZ1 (GASZ) Meiotic arrest LINE1 and IAP [104]
MAEL Meiotic arrest LINE1 and IAP [74]
FKBP6 Meiotic arrest LINE1 [105]
Hsp90α Meiotic arrest LINE1 [106, 107]
GTSF1 Meiotic arrest LINE1 and IAP [108]
HENMT1 Spermiogenic defect LINE1 and IAP [85]
Nct1/Nct2 (non-coding) fertile LINE1 [82]
EXD1 fertile LINE1 (low penetrance) [109]
Non-piRNA pathway factors
DNMT3L Meiotic arrest LINE1 and IAP [11, 75]
MORC1 Meiotic arrest LINE1 and IAP [72]
EHMT2 (G9a) Meiotic arrest Co-suppression of LINE1 [62]