Table 1.
Primary | Secondary static | Secondary NBIA | ||||
---|---|---|---|---|---|---|
Participants, (n) | 14 | 22 | 8 | |||
Median age in years (range) | 13.4 (4.5–18.1) | 10.5 (3.3–17.8) | 10.1 (4.3–17.2) | |||
GPi cells | GPe cells | GPi cells | GPe cells | GPi cells | GPe cells | |
Cells, (n) | 123 | 31 | 109 | 39 | 31 | 17 |
Median firing frequency (Hz) | 13.5 | 13.5 | 9.6 | 7 | 25 | 15.9 |
Minimum–maximum frequency (Hz) | 1–112 | 2–115 | 1–66 | 1–75 | 6–82 | 4–72 |
IQR | 8.0–29.5 | 5.1–24.3 | 3.2–23.5 | 6.0–24.4 | 12.9–38.3 | 3.3–19.4 |
GPe, globus pallidus externa; GPi, globus pallidus interna; NBIA, neuronal brain iron accumulation.