Table 1.

Baseline characteristics of 13 patients fulfilled HLH-2004 criteria

Variable	N	%
Age
Median [range]	46 [18–77]
Gender
Male/Female	10/3	77/23
Fever	10/13	77
Splenomegaly	8/12	66.7
Bi- or pancytopenia	12/13	92.3
Ferritin (ng/mL), Median [range]	5,124 [665 – 60,761]
>10,000	8/13	61.5
>50,000	6/13	46.15
Coagulopathy	5/12	41.7
LDH (U/L), Median [range]	760 [325 – 19,841]
>2.5 times	3/13	23.1
Fibrinogen (mg/dL), Median [range]	294.5 [78 – 616]
<150	3/12	25
Triglycerides (mg/dL), Median [range]	334.5 [105–599]
>268	8/12	66.7
Soluble IL-2 receptor, (pg/mL), Median [range]	2891 [35 – 39,100]
≥2400	6/8	75