Table 2.
Classification of appendiceal mucinous neoplasms and pseudomyxoma peritonei [6]
Ronnett et al. [3] | AJCC and WHO [6] | |
---|---|---|
Tumor confined to appendix | ||
Limited to mucosa | NA | Adenoma |
Low-grade/high-grade cytology | NA | Adenoma |
Positive surgical margin | NA | Adenoma |
Neoplastic epithelium in appendix wall | NA | Invasive Mucinous Adenocarcinoma |
Tumor beyond appendix | ||
Low-grade epithelium in peritoneal mucin | Disseminated peritoneal adenomucinosis (DPAM) | Low-grade mucinous adenocarcinoma |
High-grade epithelium in peritoneal mucin | Peritoneal mucinous carcinomatosis (PMCA) | High-grade mucinous adenocarcinoma |