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. 2016 Jul 1;66(Suppl 1):573–577. doi: 10.1007/s13224-016-0921-z

Table 2.

Classification of appendiceal mucinous neoplasms and pseudomyxoma peritonei [6]

Ronnett et al. [3] AJCC and WHO [6]
Tumor confined to appendix
 Limited to mucosa NA Adenoma
 Low-grade/high-grade cytology NA Adenoma
 Positive surgical margin NA Adenoma
 Neoplastic epithelium in appendix wall NA Invasive Mucinous Adenocarcinoma
Tumor beyond appendix
 Low-grade epithelium in peritoneal mucin Disseminated peritoneal adenomucinosis (DPAM) Low-grade mucinous adenocarcinoma
 High-grade epithelium in peritoneal mucin Peritoneal mucinous carcinomatosis (PMCA) High-grade mucinous adenocarcinoma