Table 1.

Demographics of patients with MPS IVA in this study.

	Category	All MPS IVA	Attenuated	Severe
N		82	17	63
Gender: male: female		39:43	7: 10	31:32
Age (years)		22.40 ± 13.13	25.28 ± 13.08	21.67 ± 13.32
* Height (%)	<10%	11.25	0.00	14.29
	<25%	21.25	0.00	26.98
	<50%	28.75	0.00	36.51
	<75%	17.50	0.00	22.22
	<90%	16.25	76.47	0.00
	above 90%	5.00	23.53	0.00
Weight (%)*	<10%	17.72	0.00	22.58
	<25%	21.52	0.00	27.42
	<50%	25.32	5.88	30.65
	<75%	18.99	35.29	14.52
	<90%	12.66	41.18	4.84
	above 90%	3.80	17.65	0.00
** Operations (%)	Spine	49.33	37.50	52.54
	Hip	20.00	37.50	15.25
	Leg (knee, femur, tibia, ankle)	52.00	37.50	55.93
	Hand	4.00	6.25	3.39
	Trachea	5.33	0.00	6.78
	Inguinal and umbilical Hernia	6.67	0.00	8.47
	Adeno and tonsillectomy	18.67	12.50	20.34
	C-section	4.00	12.50	1.69

NA: not applicable.

^*Montaño et al [33] and Tomatsu et al. [34] n = 80, 2 patients did not provide phenotype.

^**n = 75, 7 patients did not provide surgical record.