Skip to main content
. 2016 Aug 24;113(36):10127–10132. doi: 10.1073/pnas.1612594113

Table S1.

List of candidate homozygous variants in family 1 based on exome sequencing

Chr Position Reference Variant Gene Consequence Our 616 exomes Clinseq 1000 Genomes ExAC Polyphen Patient 1 Father Mother Healthy sibling
chr1 38397501 C T INPP5B c.439G>A:p.A147T 0.0045 0.0016 0 3.22E-03 Probably damaging TT CT CT CT
chr1 54371889 G A DIO1 c.459G>A:p.M153I 0.0041 0.0011 0 2.21E-03 Probably damaging AA AG AG AG
chr1 55166996 G A MROH7 c.3285+1G>A 0.0043 0 0 4.33E-04 / AA AG AG AG
chr1 63329777 G T ATG4C c.1324G>T:p.D442Y 0.0065 0.0032 0.0005 1.55E-03 Possibly damaging TT GT GT GT
chr3 39226171 G A XIRP1 c.4766C>T:p.T1589I 0.0033 0.0011 0 5.55E-03 Benign AA AG AG GG
chr3 52537419 A G STAB1 c.754A>G:p.K252E 0.0041 0.0005 0 2.26E-03 Benign GG AG AG AG
chr3 111842564 C T GCSAM c.281G>A:p.R94Q 0.0033 0 0 1.63E-05 Benign TT CT CT CC
chr3 112648018 A G CD200R1 c.539T>C:p.L180S 0.0033 0.0011 0 4.77E-03 Benign GG AG AG AA
chr3 119911827 G A GPR156 c.433C>T:p.L145F 0.0033 0 0.0014 7.40E-04 Probably damaging AA AG AG GG
chr3 126255146 C T CHST13 c.130C>T:p.L44F 0.0033 0 0 3.43E-03 Benign TT CT CT CC
chr3 127983506 C T EEFSEC c.668C>T:p.P223L 0.0049 0.0021 0.0005 1.97E-03 Probably damaging TT CT CT CC
chr5 5463514 C T KIAA0947 c.4067C>T:p.T1356I 0.0042 0 0 0 Benign TT CT CT CT
chr5 14690368 T C FAM105B c.815T>C:p.L272P 0.0025 0 0 0 Probably damaging CC CT CT CT
chr6 131179287 C T EPB41L2 c.2548G>A:p.G850R 0.0041 0.0016 0 2.02E-03 Probably damaging TT CT CT CT
chr12 10464155 C T KLRD1 c.256C>T:p.R86W 0.0049 0 0 5.69E-05 Probably damaging TT CT CT CT
chr13 53603108 T A OLFM4 c.137T>A:p.F46Y 0.0033 0 0 3.60E-03 Benign AA AT AT TT
chr15 34077949 G A RYR3 c.9355G>A:p.E3119K 0.0058 0.001 0 2.47E-03 Probably damaging AA AG AG GG
chr15 43512935 C T EPB42 c.89G>A:p.S30N 0.0041 0.0011 0.0027 1.35E-03 Benign TT CT CT CT
chr16 56709804 C A MT1IP c.134C>A:p.A45E 0.0129 0 0.0046 2.25E-03 NA AA AC AC AC
chr16 57602000 C T GPR114 c.1054C>T:p.R352C 0.0041 0 0.0005 9.03E-04 Probably damaging TT CT CT CT
chr19 1117467 G A SBNO2 c.1559C>T:p.A520V 0.015 0 0 3.31E-05 Probably damaging AA AG AG AG

Boldface type indicates the only gene in common between family 1 and patient 2.