Table 1.
Congenital heart disease in the total cohort
| All (n =134) | Unrepaired (n = 83) | Repaired (n = 51) | |
|---|---|---|---|
| ASD±PAPVR | 28 (21) | 22 (79) | 6 (21) |
| VSD and/or PDA | 56 (42) | 37 (66) | 19 (34) |
| ASD+VSD and/or PDA | 19 (14) | 12 (63) | 7 (37) |
| Complete AVSD | 13 (10) | 5 (38) | 8 (62) |
| Nonrepaired functional univentricular heart | 1 (1) | 1 (100) | … |
| Miscellaneous | 17 (13) | 6 (35) | 11 (65) |
| Group 5 PH: MAPCAs | 2 | 1 | 1 |
| Not-classifiable PAH-CHD | 15 (11) | ||
| Aortic coarctation | 2 | 0 | 2 |
| Repaired TAPVR | 1 | 0 | 1 |
| Unilateral absence of PA | 5 | 4 | 1 |
| Scimitar syndrome | 1 | 1 | 0 |
| Neonatally repaired TGA±VSD | 6 | 0 | 6 |
Note
Data are presented as no. (%) of patients; percentages are within column for “All” and within row for “Unrepaired” and “Repaired.” ASD: atrial septal defect; AVSD: atrioventricular septal defect; MAPCAs: major aortopulmonary collateral arteries; PA: pulmonary artery; PAH-CHD: pulmonary arterial hypertension associated with congenital heart disease; PAPVR: partial anomalous pulmonary venous return; PDA: patent arterial duct; PH: pulmonary hypertension; TAPVR: total anomalous pulmonary venous return; TGA: transposition of the great arteries; VSD: ventricular septal defect.