Skip to main content
. 2016 Jul 1;10(7):TE01–TE10. doi: 10.7860/JCDR/2016/21443.8210

[Table/Fig-16]:

Truncus arteriosus.

Subtypes: Collett and Edwards classification [18] graphic file with name jcdr-10-TE01-g015.jpg
Type I = pulmonary trunk arises from proximal truncus
Type II and III= no pulmonary trunk; branch PA arise from posterior and lateral mid-segments of truncus
Type IV=pulmonary circulation dependent on MAPCAs.
Incidence 1% of CHD. 1 in 11,000 live births(10–5)
Association [13] Right aortic arch, interrupted aortic arch, coarctation, PDA Coronary artery anomalies(stenotic coronary ostia, abnormal branching and course) Unilateral absence of pulmonary artery
Syndromes DiGeorge syndrome Pierre Robin syndrome
Imaging features Plain Moderate cardiomegaly with narrow base High cephalic origin of PA Right aortic arch Depressed diaphragm Thymic atrophy
Imaging features specific Echo large truncus, large VSD and a large echogenic truncal valve with fibrous continuity with anterior mitral leaflet MRI -similar findings
Management Primary repair: done in first week of life; consists of VSD closure and placement of valve conduit between RV and PA (Rastelli procedure)