[Table/Fig-20]:
Infracardiac Tapvc | Pathway of pulmonary venous return: Common pulmonary venous channel drains into portal vein, ductus venosus, hepatic vein or IVC by crossing the diaphragm through esophageal hiatus | |
Incidence [13] | Accounts for 20% of TAPVC patients. Marked male preponderance with M:F ratio of 4:1. Most of infracardiac TAPVC are obstructed. Hence it is considered as one of the paediatric cardiac emergency. | |
Association | ASD/PFO | |
Syndromes | ||
Imaging features Plain | Normal or mild cardiomegaly | Pulmonary oedema features (diffuse reticular pattern and Kerley B lines) |
Imaging features specific | Echo - dilated descending vein passing through diaphragm and draining into systemic veins. MRI best suited for post-op follow-up CT useful in features of obstruction on ECHO with unclear site of obstruction |
|
Management [13] | Surgical: Large vertical anastomosis between common pulmonary venous channel and LA with ligation of common channel above the diaphragm |