[Table/Fig-8b]:
PA-VSD.
| Frequency [13] | 2.5-3.4% of all CHD. M>F. | ||
| Association | ASD/PFO Origin of aorta from RV | ||
| Syndromes | Velo-cardio-facial syndrome DiGeorge syndrome | ||
| Imaging features Plain | Normal or mild cardiomegaly (Boot shaped heart) | Pulmonary oligemia | Hyper translucent lung fields |
| Imaging features specific | Echo mal-aligned VSD with overriding of aorta, pulmonary atresia MRI can depict all findings CT preferred for coronary artery anomalies and collaterals | ||
| Management | Medical: Start PGE1 to maintain ductal patency Surgical:
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