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. Author manuscript; available in PMC: 2016 Sep 15.
Published in final edited form as: J Magn Reson Imaging. 2012 Oct 10;37(4):974–980. doi: 10.1002/jmri.23852

Table 1.

Fluid NMR Spectroscopy Result

Patients Patient 1 Patient 2 Patient – type I* Patient – type II**
Body fluid S-Ado SAICAr S-Ado SAICAr S-Ado SAICAr S-Ado SAICAr
Urine (μmol/mmol creatinine) 200 212 288 291 683 213 690 240
Plasma (μmol/l) ND ND ND ND ND ND
CSF (μmol/l) 120 117 305 436 368 188 1130 390

ND, nondetectable; SAICAr, succinylaminoimidazole carboxamide riboside; S-Ado, succinyladenosine.

*

Published as patient #2 in Ref 15.

**

Published as patient #3 in Ref 15.