Figure 1.

Facial and intraoral features of ectodermal dysplasia of the probands of four families. Facial features include abnormal hair distribution of the scalp, low hairline with forehead fuzziness, broad and low nose bridge, columella extending with age, thick lips, slight ocular hypertelorism, and downward slanting of the palpebral fissures. Unaffected relative in these families did not have these features. All affected family member had severe oligodontia of primary and permanent teeth with particular loss of the upper lateral incisors and lower anterior teeth, accompanied by large gaps and reduction of the alveolar bone height.