I |
All bones and digits present, brachydactyly and syndactyly |
Normal |
Bones present, brachydactyly or syndactyly |
Syndactyly release |
IIA |
≥2 fingers. Normal thumb, hypoplastic fingers |
Normal |
Hypoplastic, syndactyly |
Nonvascularized toe phalanx transfers, ablation, or stabilization |
IIB |
Functional border digits, variable central nubbins |
Normal |
Present, variable hypoplasia and stability |
Surgery rarely indicated |
IIC |
“Spoon hand,” thumb conjoined with hypoplastic ulnar digits |
Present (± stability) |
Hypoplastic, clinodactyly |
Variable |
IIIA |
Monodactyly |
Normal |
Absent |
Vascularized toe-to-hand transfer |
IIIB |
Monodactyly |
Hypoplastic and/or unstable |
Absent |
Variable, vascularized toe-to-hand transfer, thumb stabilization, thumb lengthening |
IVA |
Peromelic, wrist mobility |
Absent |
Absent |
|
IVB |
Peromelic, no wrist mobility |
Absent |
Absent |
Surgery not indicated |