Table 5.

Proposed Shanghai score system for diagnosis of Early Repolarization Syndrome

I. Clinical History
A. Unexplained cardiac arrest, documented VF or polymorphic VT	3
B. Suspected arrhythmic syncope	2
C. Syncope of unclear mechanism/unclear etiology	1
*Only award points once for highest score within this category
II. 12-Lead ECG
A. ER ≥ 0.2 mV in > 2 inferior and/or lateral ECG leads with horizontal/descending ST segment	2
B. Dynamic changes in J-point elevation (> 0.1 mV) in > 2 inferior and/or lateral ECG leads	1.5
C. ≥ 0.1 mV J-point elevation in at least 2 inferior and/or lateral ECG leads	1
*Only award points once for highest score within this category
III. Ambulatory ECG monitoring
A. Short coupled PVCs with R on ascending limb or peak of T wave	2
IV. Family History
A. Relative with definite ERS	2
B. > 2 first-degree relatives with a II.A. ECG pattern	2
C. A first-degree relative with a II.A. ECG pattern	1
D. Unexplained sudden cardiac death < 45 years in a first/second-degree relative	0.5
*Only award points once for highest score within this category
V. Genetic Test Result
A. Probable pathogenic ERS-susceptibility mutation	0.5
SCORE (Requires at least one ECG finding)
> 5 points – Probable/Definite ERS
3 – 4.5 points – Possible ERS
< 3 points – Non-Diagnostic