Figure 1.

Diagnostic features of primary pulmonary artery sarcoma (PPAS). (A) An axial section of computed tomography angiography (CTA) demonstrates subtotal obstruction of the main pulmonary artery. Despite the nearly occlusive nature of tumor, this young patient presented with a progressive history of dyspnea over 2–3 weeks; (B) extension of mass is observed within a secondary branch of the pulmonary artery; (C) magnetic resonance angiography (MRA) from the same patient demonstrates local tissue invasion; (D) continuous wave Doppler from transthoracic echocardiography confirming pulmonary hypertension provides an estimated right ventricular systolic pressure >100 mmHg prior to surgical resection.