Table 5.
Proposed Shanghai Score System for diagnosis of early repolarization syndrome.
| Points | |
|---|---|
| I. Clinical History | |
| A. Unexplained cardiac arrest, documented VF or polymorphic VT | 3 |
| B. Suspected arrhythmic syncope | 2 |
| C. Syncope of unclear mechanism/unclear etiology | 1 |
| *Only award points once for highest score within this category | |
| II. Twelve-Lead ECG | |
| A. ER ≥0.2 mV in ≥2 inferior and/or lateral ECG leads with horizontal/descending ST segment | 2 |
| B. Dynamic changes in J-point elevation (≥0.1 mV) in ≥2 inferior and/or lateral ECG leads | 1.5 |
| C. ≥0.1 mV J-point elevation in at least 2 inferior and/or lateral ECG leads | 1 |
| *Only award points once for highest score within this category | |
| III. Ambulatory ECG Monitoring | |
| A. Short-coupled PVCs with R on ascending limb or peak of T wave | 2 |
| IV. Family History | |
| A. Relative with definite ERS | 2 |
| B. ≥2 first-degree relatives with a II.A. ECG pattern | 2 |
| C. First-degree relative with a II.A. ECG pattern | 1 |
| D. Unexplained sudden cardiac death o45 years in a first- or second-degree relative | 0.5 |
| *Only award points once for highest score within this category | |
| V. Genetic Test Result | |
| A. Probable pathogenic ERS susceptibility mutation | 0.5 |
| Score (requires at least 1 ECG finding) | |
| ≥5 points: Probable/definite ERS | |
| 3–4.5 points: Possible ERS | |
| <3 points: Nondiagnostic |
ER = early repolarization; ERS = early repolarization syndrome; PVC = premature ventricular contraction; VF = ventricular fibrillation; VT = ventricular tachycardia.