Table 2.

Summary table for pancreatoblastoma

Etiology	Unknown; most cases sporadic
Incidence	Around 0.004 new cases per 100,000 population
Gender ratio	Almost equal distribution in adults
Age predilection	Most commonly in patients 1 to 8 years of age Rare cases in adults (35 cases in adults reported in literature)
Risk factors	2/3 of cases in Asian descents Occasionally associated with alterations in the Wnt signaling pathway and chromosome 11p loss of heterozygosity (LOH), Beckwith-Wiedemann syndrome and familial adenomatous polyposis
Treatment	The only curative treatment is complete resection Radiotherapy or chemotherapy may be given in some cases (higher stage)
Prognosis	In adults is uniformly poor – survival median time varies between 5 and 20 months In children the tumor is more indolent, with a better prognosis, particularly if completely resected.
Findings on imaging	Usually large, well defined, at least partially circumscribed, lobulated, and heterogeneous with solid and cystic components US: solid inseparable pancreatic mass with mixed echogenicity CT: better demonstrates calcifications MRI: heterogeneous with low to intermediate signal intensity on T1-wi and high signal on T2; better delineates intratumoral hemorrhage and necrotic areas. Enhancement is a common feature on contrast-enhanced CT and MRI.