Table 1. Variables of SScl disease activity index at presentation.

Variables	Patient 1	Patient 2
Age at presentation	28	30
Modified Rodnan skin score	30	23
Scleroderma skin aspect	Yes	Yes
Skin manifestation changes	Yes	Yes
Digital necrosis	Yes	No
Raynaud’s	Yes	Yes
Arthritis	No	Yes
DLCO disturbances less than 80%	Yes	Yes
Pulmonary artery hypertension	Yes	Yes
Lung fibrosis stage	4	0
Heart manifestations	Yes**	Yes
ESR >30	Yes	Yes
Hypocomplementemia	Yes	No

**, pericarditis in both patients. SScl, Systemic Sclerosis or Scleroderma; DLCO, diffusing capacity of the lungs for carbon monoxide; ESR, erythrocyte sedimentation rate.